Zhu X, Lian N, Cai Z
Beijing Institute of Otorhinolaryngology.
Zhonghua Er Bi Yan Hou Ke Za Zhi. 1995;30(3):157-9.
Hearing loss and CT findings of 200 ears from 102 cases with congenital malformation of inner ear were included in our study. Hearing loss was typically bilateral severe, or total deafness. 75 percent of them were found deaf within one-year-old. In addition, 47 patients' (46%) mothers were noted to have caught a cold in first trimester of pregnancy. Temporal bone abnormalties were described as five types: 1. Michel malformation, 2. Mondini malformation, 3. enlargement of the vestibular aqueducts, 4. developmental deformity of cochlear aqueduct, 5. developmental deformity of internal acoustic meatus. Most cases showed malformations of vestibule or vestibular aqueducts.
本研究纳入了102例内耳先天性畸形患者的200只耳朵的听力损失及CT表现。听力损失通常为双侧严重或全聋。其中75%在1岁内被发现失聪。此外，47例患者（46%）的母亲在孕期头三个月患过感冒。颞骨异常分为五种类型：1. 米歇尔畸形；2. 蒙迪尼畸形；3. 前庭导水管扩大；4. 蜗水管发育畸形；5. 内耳道发育畸形。大多数病例表现为前庭或前庭导水管畸形。
