Dudgeon D L, Haller J A
Surgery. 1984 Mar;95(3):371-3.
Lipoblastomatosis is a rare, fatty tumor of childhood that is usually located in the limbs. Two pediatric patients were seen with tumors that originated in the mediastinum and retroperitoneal area. The mediastinal tumor was the infiltrating form of lipoblastomatosis while the retroperitoneal tumor was the noninfiltrating type. Neither form is malignant but local recurrences are common. Both were surgically excised without sacrifice of important contiguous structures that were surrounded by tumor. There has been no recurrence 21/2 and 6 years after operation. Conservative excision of this malignant-appearing but histologically benign tumor is emphasized.
脂肪母细胞瘤病是一种罕见的儿童期脂肪性肿瘤，通常位于四肢。有两名儿科患者的肿瘤起源于纵隔和腹膜后区域。纵隔肿瘤为脂肪母细胞瘤病的浸润型，而腹膜后肿瘤为非浸润型。两种类型均非恶性，但局部复发很常见。两者均通过手术切除，未牺牲被肿瘤包围的重要相邻结构。术后2年半和6年均未复发。强调对这种看似恶性但组织学上为良性的肿瘤进行保守切除。
