Salama J, Hauw J J, Dubas F, Giroux C, Frison A, Delaporte P
Ann Med Interne (Paris). 1984;135(1):39-42.
The association of Adie's syndrome and of neuropathy of chronic evolution is not a frequent occurrence; first made known by Togi in 1967, four cases have been described ever since. The authors report two new observations: one concerns a man showing a unilateral tonic pupil associated to sensory neuropathy, raised C.S.F. protein, rarefaction of myelinated fibres with schwannian proliferation, without amyloid deposit. The other is that of a woman affected with bilateral pupillotonia, motor neuropathy of the four limbs and generalized amylosis. If the first observation is comparable to the five cases reported, the second is more questionable: the absence of amyloid deposit on three nerve biopsies and at the ciliary ganglion level does not absolutely exclude the possibility of amyloid neuropathy.
阿狄氏综合征与慢性进展性神经病变的关联并不常见；1967年由托吉首次报道，此后仅描述过4例。作者报告了两例新病例：一例是一名男性，表现为单侧强直性瞳孔，伴有感觉神经病变、脑脊液蛋白升高、有雪旺氏细胞增生的有髓纤维稀疏，无淀粉样沉积物。另一例是一名女性，患有双侧瞳孔强直、四肢运动神经病变和全身性淀粉样变性。如果第一例与已报道的5例病例相似，那么第二例则更值得怀疑：三次神经活检以及睫状神经节水平均未发现淀粉样沉积物，但这并不能绝对排除淀粉样神经病变的可能性。
