Lapointe R, Gamache A, Paré P
Can J Surg. 1984 May;27(3):271-3.
Cystic dilatation of the biliary tree is an uncommon congenital condition, most often discovered in infancy. It should be suspected in an adult who has a history, over a long period, of intermittent pain in the right upper quadrant, episodes of jaundice or cholangitis, or both, and has a palpable mass in the right hypochondrium. Ultrasonography and especially endoscopic retrograde cholangiopancreatography allow the biliary cyst to be diagnosed preoperatively more often than previously. The authors describe the case of a 60-year-old woman with congenital cystic dilatation of extra- and intrahepatic bile ducts with cystlithiasis that followed an unusual course. Of the various theories of causation, Babbitt 's is now the most widely accepted, especially since the advent of endoscopic retrograde cholangiopancreatography. The presence of stones is an uncommon and late complication. The treatment is surgical, excision of the biliary cysts being the treatment of choice; however, Roux-en-Y choledochocystojejunostomy is performed when excision is technically impossible.
胆管囊性扩张是一种罕见的先天性疾病，多在婴儿期被发现。对于有长期右上腹间歇性疼痛、黄疸发作或胆管炎发作病史，或两者皆有，且在右季肋部可触及肿块的成年人，应怀疑此病。超声检查，尤其是内镜逆行胰胆管造影术，使术前诊断胆管囊肿的几率比以往更高。作者描述了一例60岁女性，患有肝内外胆管先天性囊性扩张并伴有胆囊结石，其病程不同寻常。在各种病因理论中，巴比特氏理论目前最为广泛接受，尤其是在内镜逆行胰胆管造影术出现之后。结石的存在是一种罕见的晚期并发症。治疗方法为手术治疗，首选切除胆管囊肿；然而，当技术上无法切除时，则施行 Roux-en-Y 胆总管囊肿空肠吻合术。
