Suarez J C, Sfaello Z M, Albarenque M, Viano J C
Childs Brain. 1984;11(2):77-86. doi: 10.1159/000120163.
The therapeutic criteria according to tomographic findings are reviewed. 10 children, 6 male and 4 female, with porencephalic congenital cysts were studied. Early symptoms began within the first 6 months of life in 9 cases, and at the age of 5 years in 1. The most frequent symptoms were: seizures in 3; motor deficit in 5; retarded psychomotor development in 7; endocranial hypertension syndrome in 7; symmetric macrocrania in 7; paresis of the motor ocular nerves in 4. Preoperative studies: X-ray films-1 each patient-showed diastasis of sutures in 6 and cranial asymmetry in 2. Electroencephalograms-6 patients-were abnormal and diffuse in 3, hipsarrhythmic in 2, and focal in 1. CT-1 each patient-showed porencephalic cysts in all the patients; ventricular dilatation in 9; a single ventricle in 1, and a shift of the midline in 5. Postoperative studies: EEG, 1 each patient; CT, 1 each patient.
8 patients underwent peritoneal shunts and 2 atrial shunts. Plastic surgery of the dysraphy was also performed. Postsurgical treatment: Rehabilitation and anti-convulsive treatment-4 patients. There were no deaths among the patients. The morbidity improved.
根据断层扫描结果回顾了治疗标准。研究了10例患有脑穿通性先天性囊肿的儿童，其中男性6例，女性4例。9例患者在出生后的前6个月内出现早期症状，1例在5岁时出现症状。最常见的症状有：3例癫痫发作；5例运动功能障碍；7例精神运动发育迟缓；7例颅内高压综合征；7例头颅增大；4例动眼神经麻痹。术前检查：每位患者均进行了X线检查，6例显示颅骨缝分离，2例显示颅骨不对称。6例患者进行了脑电图检查，3例异常且呈弥漫性，2例呈节律紊乱，1例呈局灶性。每位患者均进行了CT检查，所有患者均显示脑穿通性囊肿；9例脑室扩张；1例单脑室；5例中线移位。术后检查：每位患者均进行了脑电图和CT检查。
8例患者接受了腹腔分流术，2例接受了心房分流术。还进行了脊柱裂修补整形手术。术后治疗：4例患者进行了康复和抗惊厥治疗。患者中无死亡病例。病情有所改善。
