Plenat F, Vignaud J M, Floquet J, Leroux P, Briquel N, Morali A, Vidailhet M
Ann Pathol. 1984 Apr-May;4(2):131-6.
Report of a child with disseminated ganglioneuromatosis of the gut. The complexity of the intestinal nervous system malformation is proved by histochemical, histoenzymological and ultrastructural studies. The malformation is characterized by: hyperplasia and hypertrophy of enteric plexus and nerves bundles in the meso, high acetylcholinesterase activity, aplasia of the sympathetic innervation with the exception of perivascular plexus, qualitative and likely quantitative integrity of the endocrine digestive system. These data are compared with similar observations in the literature.
一例肠道播散性神经节瘤病患儿的报告。组织化学、组织酶学和超微结构研究证实了肠道神经系统畸形的复杂性。该畸形的特征为:中肠内肠神经丛和神经束增生肥大、乙酰胆碱酯酶活性高、除血管周围丛外交感神经支配发育不全、内分泌消化系统在质量和可能的数量上保持完整。将这些数据与文献中的类似观察结果进行了比较。