Adam Y, Boutard P, Ravasse M, Houtteville J P, Guihard J, Borel B, Delmas P
Chir Pediatr. 1984;25(1):32-6.
The authors would like to recount and discuss the case of a 14 months old child which presented a dumbbell dorsal lipoma, purely extradural with no congenital anomalies. The warning signal was the discovery of paraparesis with the regression of walking ability. The hypothesis of medullary compression by a dumbbell dorsal tumor was quickly dismissed with the discovery of a mediastinal mass on the pulmonary X-Ray. A diagnosis of the pre-operational neuroblastoma was carried out because of detection of dorsal epidural medullary compression revealed by the myelography. The testing was completed with a vertebral computed tomography, which clearly showed the extent of medullar compression, and the mediastinal tumoral development under the paravertebral muscular masses. The child was operated on at 2 fronts, vertebrally and thoraxically for an encapsulated, perfectly separable and non hemorrhaging tumor. The anatomopathological examination confirmed the diagnosis of the lipoma. It is in the resumption of the computed tomographic examination that the tumoral density measures will confirm fatty tissue with numbers of density--50. In light of the literature, we are discussing the appearance of the lipoma, entirely exceptional because of its dorsal location, its extradural and certainly its dumbbell position, with large thoraxic development. It is necessary to stress the importance of the meticulous neurological examination of the child, the diagnostical necessity of the CT scan and the importance of the avoidance of the creation of an instable vertebral lesion at the time of laminotomy. In this case only the early double surgical operation permitted the recovery of the child.
作者想要讲述并讨论一个14个月大儿童的病例,该患儿患有哑铃状背侧脂肪瘤,完全位于硬膜外,无先天性异常。警示信号是发现双下肢轻瘫且行走能力退化。随着肺部X光检查发现纵隔肿块,哑铃状背侧肿瘤压迫脊髓的假设很快被排除。由于脊髓造影显示存在硬膜背侧脊髓压迫,术前诊断为神经母细胞瘤。通过脊椎计算机断层扫描完成了检查,该检查清楚地显示了脊髓压迫的程度以及椎旁肌肉肿块下方纵隔肿瘤的发展情况。该患儿接受了脊椎和胸部两个部位的手术,切除了一个包膜完整、完全可分离且无出血的肿瘤。解剖病理学检查证实了脂肪瘤的诊断。在计算机断层扫描复查中,肿瘤密度测量结果将证实为脂肪组织,密度值为-50。根据文献,我们正在讨论该脂肪瘤的表现,因其背侧位置、硬膜外以及肯定还有其哑铃状位置且伴有较大的胸部发展,这种情况极为罕见。有必要强调对患儿进行细致神经系统检查的重要性、CT扫描的诊断必要性以及在椎板切开术时避免造成不稳定椎体病变的重要性。在这个病例中,只有早期的双手术操作才使患儿得以康复。