Germain D, Bernheim A
Pathol Biol (Paris). 1982 Nov;30(9):802-16.
Chromosome instability syndromes are defined by either an increase of chromosomal breakage or by an increase of sister chromatid exchange number, or by an increase of the two. Bloom's syndrome, Ataxia telangiectasia, Fanconi's Anemia are the main components of this group. The incidence of cancers or malignant blood diseases is high. The finding of DNA repair abnormalities in some of them and their high sensitivity to particular mutagenic agents makes those syndromes an interesting model for oncogenesis.
染色体不稳定综合征的定义是染色体断裂增加,或姐妹染色单体交换数增加,或两者都增加。布卢姆综合征、共济失调毛细血管扩张症、范科尼贫血是这一组疾病的主要组成部分。癌症或恶性血液病的发病率很高。在其中一些疾病中发现的DNA修复异常以及它们对特定诱变剂的高敏感性,使这些综合征成为肿瘤发生的一个有趣模型。