Flynn M P, Buchanan J B
South Med J. 1980 May;73(5):618-20, 626. doi: 10.1097/00007611-198005000-00020.
A case of bilateral renal artery stenosis and aneurysms in association with neurofibromatosis and hypertension is discussed and the literature is reviewed. In patients with neurofibromatosis and hypertension, the association of pheochromocytomas is well known. The association of renal of renal vascular lesions must also be recognized. In children with neurofibromatosis and hypertension, renal artery stenosis is far more common than pheochromocytoma. In adults aneurysms often accompany the renal artery stenosis. Laboratory studies, as well as most intravenous pyelograms, have been normal and, therefore, unreliable for screening. Angiography is essential in the investigation of hypertension in patients with neurofibromatosis.
本文讨论了一例双侧肾动脉狭窄和动脉瘤合并神经纤维瘤病及高血压的病例，并对相关文献进行了综述。在患有神经纤维瘤病和高血压的患者中，嗜铬细胞瘤的关联是众所周知的。肾血管病变的关联也必须得到认识。在患有神经纤维瘤病和高血压的儿童中，肾动脉狭窄远比嗜铬细胞瘤常见。在成人中，动脉瘤常伴随肾动脉狭窄。实验室检查以及大多数静脉肾盂造影结果均正常，因此对于筛查不可靠。血管造影对于神经纤维瘤病患者高血压的调查至关重要。
