人脾脏膜结合β-葡萄糖苷酶的同工酶
Isoenzymes of membrane-bound beta-glucosidase of human spleen.
作者信息
Yaqoob M, Carroll M
出版信息
Biochem J. 1980 Feb 1;185(2):541-3. doi: 10.1042/bj1850541.
Abstract
Normal human spleen contains two forms of membrane-bound beta-glucosidase, distinguishable by their thermostability and kinetic properties. The spleen from a patient with adult Gaucher's disease was deficient in the major, thermolabile, form of the enzyme.
摘要
正常人类脾脏含有两种膜结合型β-葡萄糖苷酶，可通过它们的热稳定性和动力学特性加以区分。一名成年戈谢病患者的脾脏中，主要的热不稳定型酶存在缺陷。
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本文引用的文献
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Identity of 'acid' beta-glucosidase and glucocerebrosidase in human spleen.人脾脏中“酸性”β-葡萄糖苷酶与葡糖脑苷脂酶的同一性
Biochem J. 1973 Nov;136(3):721-9. doi: 10.1042/bj1360721.
3
Solubilization of glucocerebrosidase from human placenta and demonstration of a phospholipid requirement for its catalytic activity.从人胎盘中溶解葡萄糖脑苷脂酶并证明其催化活性对磷脂的需求。
Biochem Biophys Res Commun. 1976 Aug 23;71(4):1048-53. doi: 10.1016/0006-291x(76)90760-9.
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Gaucher disease: isolation and comparison of normal and mutant glucocerebrosidase from human spleen tissue.戈谢病：从人脾脏组织中分离并比较正常和突变的葡萄糖脑苷脂酶
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