Hertz I H, Keller R J
AJR Am J Roentgenol. 1981 Jan;136(1):204-5. doi: 10.2214/ajr.136.1.204.
Paroxysmal nocturnal hemoglobinuria (PNH) is a chronic hemolytic anemia of unknown etiology associated with morning hemoglobinuria, variable acholuric jaundice, and striking hemosiderinuria, all signs of hemolysis. Paroxysmal nocturnal hemoglobinuria with infarction and hemorrhage of the gut leading to emergency surgery has been reported [1]; a history of thrombosis may be found before PNH is diagnosed [2]. We describe the radiographic findings in the small bowel of a patient with paroxysmal nocturnal hemoglobinuria during an episode of moderately severe abdominal symptoms. Ours is the second reported case using barium study.
阵发性睡眠性血红蛋白尿(PNH)是一种病因不明的慢性溶血性贫血,伴有晨起血红蛋白尿、可变的无胆色素尿性黄疸和显著的含铁血黄素尿,这些都是溶血的表现。已有报道阵发性睡眠性血红蛋白尿患者出现肠道梗死和出血并导致急诊手术[1];在阵发性睡眠性血红蛋白尿被诊断之前可能会发现血栓形成史[2]。我们描述了一名阵发性睡眠性血红蛋白尿患者在中度严重腹部症状发作期间小肠的影像学表现。我们的病例是第二例使用钡剂造影研究报道的病例。