Halphen C, Beaufils P, Azancot I, Baudouy P, Manne B, Slama R
Arch Mal Coeur Vaiss. 1981 Sep;74(9):1113-8.
The authors report a case of arrhythmogenic right ventricular dysplasia in a 61year old male with a 9 year history of recurrent ventricular tachycardia with a left bundle branch block configuration and without any signs of cardiac failure. A right ventricular angiography showed morphological changes suggestive of Uhl's anomaly and left ventricular angiography showed segmental wall dysfunction. In the absence of coronary artery disease, this case raises the questions of left ventricular extension of right ventricular dysplasia and of the value of left ventricular angiography in adult forms of Uhl's anomaly.
作者报告了一例61岁男性致心律失常性右心室发育不良病例,该患者有9年复发性室性心动过速病史,呈左束支传导阻滞形态,且无任何心力衰竭迹象。右心室血管造影显示形态学改变提示乌尔畸形,左心室血管造影显示节段性室壁功能障碍。在无冠状动脉疾病的情况下,该病例引发了关于右心室发育不良左心室扩展以及左心室血管造影在成人型乌尔畸形中的价值的问题。