Gomperts E D, Malekzadeh M H, Fine R N
Thromb Haemost. 1981 Oct;46(3):626-8.
Hemodialysis was initiated in a mild-moderate hemophiliac at 15 years of age. Hematuria had been a frequent and persisting feature from the age of five years without documented cause. Anemia and proteinuria was first detected at 13 years. A cadaver donor renal transplant was carried out after three months of hemodialysis. Massive intravesical bleeding complicated the immediate post-transplantation period. The allograft rejected after three months and the patient was maintained for eight years on home hemodialysis. A second cadaver donor allograft was carried out at 23 years of age. Again, massive intravesical hemorrhage was a problem post-transplant. The allograft is currently functioning 27 months post-transplant. Factor VIIIc activities have fluctuated between 5% and 40% in the absence of factor infusions.
一名15岁的轻中度血友病患者开始接受血液透析。自5岁起,患者便经常出现血尿且持续存在,病因不明。13岁时首次检测到贫血和蛋白尿。血液透析3个月后进行了尸体供肾移植。移植术后即刻出现大量膀胱内出血并发症。3个月后移植肾发生排斥反应,患者接受家庭血液透析维持了8年。23岁时进行了第二次尸体供肾移植。移植后同样出现大量膀胱内出血问题。目前该移植肾在移植后27个月仍在发挥功能。在未输注凝血因子的情况下,凝血因子VIIIc活性在5%至40%之间波动。