慢性复发性血栓性血小板减少性紫癜中异常大的血浆因子VIII：血管性血友病因子多聚体 - Suppr

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超能文献

Unusually large plasma factor VIII: von Willebrand factor multimers in chronic relapsing thrombotic thrombocytopenic purpura.

作者信息

Moake J L, Rudy C K, Troll J H, Weinstein M J, Colannino N M, Azocar J, Seder R H, Hong S L, Deykin D

出版信息

N Engl J Med. 1982 Dec 2;307(23):1432-5. doi: 10.1056/NEJM198212023072306.

DOI:10.1056/NEJM198212023072306

PMID:6813740

Abstract

摘要

相似文献

Unusually large plasma factor VIII: von Willebrand factor multimers in chronic relapsing thrombotic thrombocytopenic purpura.慢性复发性血栓性血小板减少性紫癜中异常大的血浆因子VIII：血管性血友病因子多聚体

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Effects of fresh-frozen plasma and its cryosupernatant fraction on von Willebrand factor multimeric forms in chronic relapsing thrombotic thrombocytopenic purpura.新鲜冰冻血浆及其冷上清组分对慢性复发性血栓性血小板减少性紫癜中血管性血友病因子多聚体形式的影响。

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Chronic relapsing thrombotic thrombocytopenic purpura: three case reports and update of the pathogenesis and therapeutic modalities.慢性复发性血栓性血小板减少性紫癜：三例报告及发病机制与治疗方式的更新

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Chronic relapsing thrombotic thrombocytopenic purpura in infants with large von Willebrand factor multimers during remission.缓解期伴有大血管性血友病因子多聚体的婴儿慢性复发性血栓性血小板减少性紫癜

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Thrombotic thrombocytopenic purpura: successful treatment unlocks etiologic secrets.血栓性血小板减少性紫癜：成功治疗揭开病因之谜。

Mayo Clin Proc. 1989 Aug;64(8):956-61. doi: 10.1016/s0025-6196(12)61223-3.

von Willebrand factor abnormalities and endothelial cell perturbation in a patient with acute thrombotic thrombocytopenic purpura.一名急性血栓性血小板减少性紫癜患者的血管性血友病因子异常与内皮细胞紊乱

Am J Med Sci. 1986 Jan;291(1):47-50. doi: 10.1097/00000441-198601000-00009.

Abnormalities of von Willebrand factor multimers in thrombotic thrombocytopenic purpura and the hemolytic-uremic syndrome.血栓性血小板减少性紫癜和溶血尿毒综合征中血管性血友病因子多聚体的异常。

Am J Med. 1989 Sep;87(3N):9N-15N.

The detection of a platelet-agglutinating factor in thrombotic thrombocytopenic purpura.血栓性血小板减少性紫癜中血小板凝集因子的检测。

Ann Intern Med. 1984 Nov;101(5):589-93. doi: 10.7326/0003-4819-101-5-589.

Aetiology and pathogenesis of thrombotic thrombocytopenic purpura and haemolytic uraemic syndrome: the role of von Willebrand factor-cleaving protease.血栓性血小板减少性紫癜和溶血尿毒综合征的病因及发病机制：血管性血友病因子裂解蛋白酶的作用

Best Pract Res Clin Haematol. 2001 Jun;14(2):437-54. doi: 10.1053/beha.2001.0142.

von Willebrand factor-cleaving protease in thrombotic thrombocytopenic purpura and the hemolytic-uremic syndrome.血栓性血小板减少性紫癜和溶血尿毒综合征中的血管性血友病因子裂解蛋白酶

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