Fuller P, Newcombe F, Ounsted C
Arch Neurol. 1983 Mar;40(3):165-8. doi: 10.1001/archneur.1983.04050030059011.
A boy with severe quadriplegia who neither recognized nor uttered speech sounds acquired language. Until the age of 6 years he was considered to be of severely subnormal intelligence. At age 6 years 9 months he was introduced to a manual sign system. Subsequently he was able to read, write, converse, and produce imaginative stories. Attention and memory were unimpaired and affective and social responsiveness developed appropriately. The case history demonstrates the selective effects of brain lesions that, despite extensive damage, may spare functional systems necessary for cognitive and linguistic development. It highlights the difficulty in diagnosing and evaluating the intellectual and affective potential of a multihandicapped child without functional hearing or speech and emphasizes the importance of sign language as a communication channel and prerequisite for the acquisition of reading and writing skills.
一名患有严重四肢瘫痪的男孩,既无法识别也无法发出语音,却学会了语言。在6岁之前,他被认为智力严重低于正常水平。6岁9个月时,他开始接触一种手势语系统。随后,他能够阅读、写作、交谈并创作富有想象力的故事。他的注意力和记忆力未受损害,情感和社交反应也得到了适当发展。该病例史表明,尽管大脑损伤广泛,但脑损伤可能会选择性地保留认知和语言发展所需的功能系统。它凸显了在诊断和评估没有功能性听力或言语的多重残疾儿童的智力和情感潜力方面的困难,并强调了手语作为一种交流渠道以及获取读写技能的先决条件的重要性。