Niewiadomska M, Wochnik-Dyjas D, Kostrzewska E, Gregor A
Neurol Neurochir Pol. 1978 May-Jun;12(3):219-27.
In a material of 28 patients with acute intermittent porphyria and 2 with mixed porphyria neurological disturbances occurring in acute attach and the degree of their persistence during remission were analysed. The obtained results indicate that the symptoms of acute attach are neurogenic. In the acute phase of the disease a reversible disturbance of function develops in the first place in the nerve fibres with acetylcholine-type of impulse transmission. Clinically detectable permanent signs of polyneuropathy were observed only in some cases with most severe and prolonged acute attack.
对28例急性间歇性卟啉病患者和2例混合型卟啉病患者的资料进行分析，观察急性发作时出现的神经功能障碍及其缓解期的持续程度。结果表明，急性发作的症状是神经源性的。在疾病的急性期，首先在具有乙酰胆碱型冲动传递的神经纤维中出现可逆性的功能障碍。仅在一些急性发作最严重且持续时间最长的病例中观察到临床上可检测到的多发性神经病的永久性体征。
