Bass S, Connon J J, Ho C S
Gastroenterology. 1983 Jun;84(6):1592-6.
Two female adolescents with cystic fibrosis were investigated by endoscopic retrograde cholangiography for recurrent abdominal pain. The cholangiogram of 1 patient demonstrated multiple irregular filling defects throughout the biliary tree representing thickened bile and mucus as well as stones. The cholangiogram of the other case illustrated cystic dilatation of the intrahepatic bile ducts with intrahepatic cholelithiasis as well as extensive irregularities of the smaller proximal ductules secondary to recurrent cholangitis or focal biliary cirrhosis, or both. Endoscopic papillotomy resulted in drainage of tenacious bile and mucus and stones in both cases. Sustained clinical improvement did not follow papillotomy in either case, whereas radiologic improvement was demonstrated in 1 case.
两名患有囊性纤维化的女性青少年因反复腹痛接受了内镜逆行胆管造影检查。其中1例患者的胆管造影显示整个胆管树有多个不规则充盈缺损，代表胆汁和黏液增厚以及结石。另一例患者的胆管造影显示肝内胆管囊性扩张伴肝内胆结石，以及由于复发性胆管炎或局灶性胆汁性肝硬化或两者兼有导致的较小近端胆管广泛不规则。两例患者经内镜乳头切开术后均排出了黏稠的胆汁、黏液和结石。两例患者术后临床症状均未持续改善，而其中1例显示出影像学改善。
