Blair W F, Shurr D G, Buckwalter J A
J Pediatr Orthop. 1983 Feb;3(1):37-40. doi: 10.1097/01241398-198302000-00007.
Function is the most important consideration in the evaluation of patients with congenital ulnar deficiency. The upper extremity function of 8 patients with ulnar deficiency was evaluated. None of these patients had been treated with surgical procedures directed to the elbow, forearm, or wrist. The functional criteria included: (a) active ranges of elbow, forearm, and wrist motion, (b) power grip, (c) prehension, (d) dexterity, and (e) a patient's activities questionnaire. The averaged total active range of joint motion was 229 degrees or 46% of predicted normal active motion. Power grip averaged 27% of the contralateral extremity, and prehension tests were generally well performed. Timed tests were completed an average of 11.6 s slower than the contralateral control hand. Our patients did not report any deficiencies in bimanual activities. Patients performed most poorly when their congenital anomaly included radiohumeral synostosis or congenital absence, deformity, or contracture of the ipsilateral digits. The radiographic appearances or classification of the ulnar deficiency, in the absence of radiohumeral synostosis, did not correlate well with patient function.
功能是评估先天性尺骨缺如患者时最重要的考量因素。对8例尺骨缺如患者的上肢功能进行了评估。这些患者均未接受针对肘部、前臂或腕部的外科手术治疗。功能标准包括：(a) 肘、前臂和腕关节的主动活动范围，(b) 强力握力，(c) 抓握能力，(d) 灵活性，以及(e) 患者活动问卷。关节活动的平均总主动范围为229度，即预测正常主动活动的46%。强力握力平均为对侧肢体的27%，抓握测试总体表现良好。计时测试完成时间平均比对侧对照手慢11.6秒。我们的患者未报告双手活动有任何缺陷。当先天性畸形包括桡肱关节融合或同侧手指先天性缺如、畸形或挛缩时，患者的表现最差。在没有桡肱关节融合的情况下，尺骨缺如的影像学表现或分类与患者功能的相关性不佳。
