Cazzaniga M, Herraiz Sarachaga I, Cayré R, Bermúdez Cañete R, Maitre Azcárate M, Quero Jiménez M, Merino Batres G
An Esp Pediatr. 1983 Jan;18(1):10-9.
Clinical findings are reported in 5 cases of anomalous left coronary artery originating from pulmonary trunk, with reference of ventricular function evaluated through echocardiographic and angio-haemodynamic methods. All patients were catheterized between 7 and 8 months of age. Left atrial and ventricular dilatation, diminished shortening of minor diameter and free wall thickness and septum normal values were obtained by echocardiography. Quantitative angiography of left ventricle demonstrated an elevation of end-diastolic volumes (mean values: 270% of predicted normal). The ejection phase indexes are diminished. The left ventricular mass/end-diastolic volume ratio was low in all cases. Myocardial imaging with thallium-201 demonstrated perfusion defect in lateral area of left ventricle in one patient. The electrocardiographic signs of myocardial necrosis support the diagnosis, and the echocardiographic and isotopic studies may contribute to it. The angio-haemodynamic method corroborate the diagnosis, and the myocardial pump function evaluation may help to decide the most appropriate treatment for this anomaly.
报告了5例起源于肺动脉干的异常左冠状动脉病例的临床发现，并参考了通过超声心动图和血管血液动力学方法评估的心室功能。所有患者均在7至8个月大时接受了心导管检查。通过超声心动图获得了左心房和心室扩张、短径缩短减少、游离壁厚度和室间隔正常数值。左心室定量血管造影显示舒张末期容积升高（平均值：预测正常值的270%）。射血期指标降低。所有病例的左心室质量/舒张末期容积比值均较低。一名患者用铊-201进行心肌显像显示左心室外侧区域存在灌注缺损。心肌坏死的心电图征象支持诊断，超声心动图和同位素研究可能有助于诊断。血管血液动力学方法证实了诊断，心肌泵功能评估可能有助于确定针对这种异常情况的最合适治疗方法。
