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假性假甲状旁腺功能减退症与嗜铬细胞瘤。是关联还是巧合?

Pseudopseudohypoparathyroidism and pheochromocytoma. Association or coincidence?

作者信息

Reeves R A, Kiss J E, Meess M, Levey G S, Shapiro A P

出版信息

Arch Intern Med. 1983 Aug;143(8):1619.

PMID:6870447
Abstract

We saw a patient who had a pheochromocytoma producing hypertension along with clear evidence of pseudopseudohypoparathyroidism (PPHP). Although PPHP does not have the biochemical features of hypocalcemia and elevated parathyroid hormone levels as seen in pseudohypoparathyroidism, it seems from this case to share the potential for multiple endocrine neoplasia seen in a number of metabolic disorders in which pheochromocytoma may be a prominent manifestation.

摘要

我们接诊了一位患有嗜铬细胞瘤并伴有高血压的患者,同时有明确的假假性甲状旁腺功能减退症(PPHP)证据。尽管PPHP不像假性甲状旁腺功能减退症那样具有低钙血症和甲状旁腺激素水平升高的生化特征,但从这个病例来看,它似乎与多种代谢紊乱中所见的多发性内分泌肿瘤有共同的潜在关联,在这些代谢紊乱中嗜铬细胞瘤可能是一个突出表现。

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