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假性假甲状旁腺功能减退症与嗜铬细胞瘤。是关联还是巧合?

Pseudopseudohypoparathyroidism and pheochromocytoma. Association or coincidence?

作者信息

Reeves R A, Kiss J E, Meess M, Levey G S, Shapiro A P

出版信息

Arch Intern Med. 1983 Aug;143(8):1619.

PMID:6870447
Abstract

We saw a patient who had a pheochromocytoma producing hypertension along with clear evidence of pseudopseudohypoparathyroidism (PPHP). Although PPHP does not have the biochemical features of hypocalcemia and elevated parathyroid hormone levels as seen in pseudohypoparathyroidism, it seems from this case to share the potential for multiple endocrine neoplasia seen in a number of metabolic disorders in which pheochromocytoma may be a prominent manifestation.

摘要

我们接诊了一位患有嗜铬细胞瘤并伴有高血压的患者,同时有明确的假假性甲状旁腺功能减退症(PPHP)证据。尽管PPHP不像假性甲状旁腺功能减退症那样具有低钙血症和甲状旁腺激素水平升高的生化特征,但从这个病例来看,它似乎与多种代谢紊乱中所见的多发性内分泌肿瘤有共同的潜在关联,在这些代谢紊乱中嗜铬细胞瘤可能是一个突出表现。

相似文献

1
Pseudopseudohypoparathyroidism and pheochromocytoma. Association or coincidence?假性假甲状旁腺功能减退症与嗜铬细胞瘤。是关联还是巧合?
Arch Intern Med. 1983 Aug;143(8):1619.
2
Acromegaly, hyperparathyroidism, and pheochromocytoma in the same patient. A multiple endocrine disorder.同一患者患肢端肥大症、甲状旁腺功能亢进和嗜铬细胞瘤。一种多发性内分泌疾病。
Arch Intern Med. 1981 Oct;141(11):1521-2.
3
Pheochromocytoma.嗜铬细胞瘤
J Ky Med Assoc. 2001 Nov;99(11):487-92.
4
[Bilateral adrenal pheochromocytoma].[双侧肾上腺嗜铬细胞瘤]
Actas Urol Esp. 1998 Apr;22(4):355-8.
5
[Successfully treated case of pheochromocytoma presenting continuous hypertension].
Saishin Igaku. 1967 Nov 10;22(11):2533-43.
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[Orthostatic hypotension: an unusual manifestation of pheochromocytoma].[直立性低血压:嗜铬细胞瘤的一种罕见表现]
Rev Med Chil. 2003 Dec;131(12):1429-33.
7
[A case of composite pheochromocytoma-ganglioneuroblastoma in the adrenal gland with primary hyperparathyroidism].肾上腺复合性嗜铬细胞瘤-神经母细胞瘤合并原发性甲状旁腺功能亢进1例
Hinyokika Kiyo. 2003 May;49(5):269-72.
8
Hypertension and pheochromocytoma.高血压与嗜铬细胞瘤。
J Clin Gastroenterol. 1983 Dec;5(6):553.
9
[Pheochromocytoma as a removable cause of arterial hypertension].[嗜铬细胞瘤作为可消除的动脉高血压病因]
Wiad Lek. 1968 May 1;21(9):785-8.
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[Paresthetic notalgia and multiple endocrine neoplasia type 2a (Sipple's syndrome): 3 cases].[感觉异常性疼痛和2a型多发性内分泌腺瘤病(西普尔综合征):3例]
Ann Dermatol Venereol. 1999 Jun-Jul;126(6-7):522-4.

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