Segura Martín M, Lorenzo Romero J G, Santiago Salinas Sánchez A, Hernández Millán I, Martínez Martín M, Atienzar Tobarra M, Virseda Rodríguez J A
Servicio de Urología, Hospital General de Albacete.
Actas Urol Esp. 1998 Apr;22(4):355-8.
Presentation of one case of bilateral suprarenal pheochromocytoma as early clinical evidence of a type 2 MEN, which at the time of diagnosis was a bilateral lesion. The presentation form was a picture of shock with HBP. Labetalol i.v. was used for initial control and phenoxybenzamine in the pre-operative. Diagnosis was achieved by biochemical (metanephrine) and radiological (CAT) testing. The patient was managed with bilateral suprarenalectomy through a single, anterior incision and abdominal cavity examination. The investigation of the remaining conditions that conform this syndrome was continued and a familial routine study implemented.
一例双侧肾上腺嗜铬细胞瘤作为2型多发性内分泌腺瘤病的早期临床证据的病例报告，诊断时为双侧病变。表现形式为伴有高血压的休克状态。静脉注射拉贝洛尔用于初始控制，术前使用酚苄明。通过生化（甲氧基肾上腺素）和放射学（计算机断层扫描）检查确诊。患者通过单一前入路切口行双侧肾上腺切除术及腹腔探查进行治疗。继续对符合该综合征的其他情况进行调查并开展家族常规研究。
