Doppman J L, Cornblath M, Dwyer A J, Adams A J, Girton M E, Sidbury J
J Comput Assist Tomogr. 1982 Feb;6(1):67-71. doi: 10.1097/00004728-198202000-00009.
Glycogen, in concentrations encountered in von Gierke's disease, has computed tomography (CT) attenuation coefficients in the 50 to 70 Hounsfield unit (HU: 1,000 scale) range and accounts for the increased density of the liver. However, in eight patients with Type I glycogen storage disease, simultaneous hepatic infiltration with fat and glycogen led to a range of liver CT densities from 13 to 80 HU. Fatty infiltration may facilitate the demonstration of hepatic tumors in older patients with this disease. Half the patients showed increased attenuation coefficients of the renal cortex, indicating glycogen deposition in the kidneys.
在冯·吉尔克病中所见到的糖原浓度下，其在计算机断层扫描（CT）中的衰减系数在50至70亨氏单位（HU：1000刻度）范围内，这解释了肝脏密度的增加。然而，在8例I型糖原贮积病患者中，肝脏同时存在脂肪和糖原浸润，导致肝脏CT密度范围为13至80 HU。脂肪浸润可能有助于在患有这种疾病的老年患者中显示肝脏肿瘤。半数患者肾皮质的衰减系数增加，表明肾脏中有糖原沉积。
