Packer R J, Cornblath D R, Gonatas N K, Bruno L A, Asbury A K
Neurology. 1980 May;30(5):492-6. doi: 10.1212/wnl.30.5.492.
A 20-year-old woman developed ataxia, extrapyramidal movements, myoclonus, and progressive dementia. Brain biopsy disclosed status spongiosus, diagnostic of Creutzfeldt-Jakob disease; this is the youngest spontaneous case ever reported. Creutzfeldt-Jakob disease can occur in young adulthood.
一名20岁女性出现共济失调、锥体外系运动、肌阵挛和进行性痴呆。脑活检显示海绵状变性,诊断为克雅氏病;这是有报道以来最年轻的自发病例。克雅氏病可发生于成年早期。