Grimwood R, Arroyave C M, Weston W L, Aeling J L
Arch Dermatol. 1980 Sep;116(9):1045-7.
Herpes gestationis (HG) is a rare, blistering disease of pregnancy and the puerperium that has immunologic findings of C3 with or without IgG deposited in a linear, band-like distribution along the dermoepidermal basement membrane zone (BMZ). A circulating IgG factor has been demonstrated that will fix complement by the classic pathway in vitro. This study involves a patient who had classic HG with C3 at the BMZ, and who had a circulating factor with activity via the alternative complement pathway similar to the previously described C3 nephritic factor found in patients with partial lipodystrophy, systemic lupus erythematosus, and membranoproliferative glomerulonephritis. Like the C3 nephritic factor, the activity was detected in IgG fractions of serum samples.
妊娠疱疹(HG)是一种罕见的妊娠和产褥期水疱性疾病,其免疫学表现为C3,IgG可呈线性、带状分布沉积于真皮表皮基底膜带(BMZ),也可不沉积。已证实存在一种循环IgG因子,该因子在体外可通过经典途径激活补体。本研究涉及一名患者,该患者患有典型的HG,BMZ处有C3沉积,且有一种循环因子,其通过替代补体途径发挥作用,类似于先前在部分脂肪营养不良、系统性红斑狼疮和膜增生性肾小球肾炎患者中发现的C3肾炎因子。与C3肾炎因子一样,该活性在血清样本的IgG组分中被检测到。