Fox B, Seed W A
Thorax. 1980 Aug;35(8):570-80. doi: 10.1136/thx.35.8.570.
We described three cases of eosinophilic pneumonia of unknown aetiology investigated clinically and by lung biopsy. The illnesses lasted between six and 20 weeks and consisted of cough, dyspnoea, malaise, and in two cases prolonged pyrexia. All had blood eosinophilia and chest radiographs showing widespread bilateral shadowing; in two cases this had a characteristic peripheral distribution. One patient recovered spontaneously and the other two responded to steroids, with disappearance of pyrexia within 12 hours and radiological clearing within 14 days. Lung function tests during the acute illness showed volume restriction or gas transfer defects or both in two cases. After remission all three showed abnormalities if small airways function. Lung biopsies performed during the acute illness were examined histologically and by transmission electron microscopy, and in two cases by immunofluorescence. There was both intra-alveolar and interstitial eosinophilic pneumonia with bronchiolitis obliterans, microgranulomata, and a vasculitis. Electron microscopy showed numerous eosinophils, many degranulated, and macrophages with phagocytosed eosinophilic granules and intracytoplasmic inclusions. In one case IgM, IgG, and IgA were demonstrated in the bronchial walls and interstitium. No IgE or complement was present. We believe that eosinophil granules are responsible for the tissue damage and fever and suggest mechanisms for this and for the response to steroid therapy.
我们描述了3例病因不明的嗜酸性粒细胞性肺炎,对其进行了临床研究及肺活检。病程持续6至20周,症状包括咳嗽、呼吸困难、不适,其中2例有长期发热。所有患者均有血液嗜酸性粒细胞增多,胸部X线片显示双侧广泛阴影;2例有特征性的外周分布。1例患者自行康复,另外2例对类固醇治疗有反应,发热在12小时内消退,影像学表现14天内恢复正常。急性发病期肺功能检查显示,2例有肺容积受限或气体交换障碍或两者皆有。缓解后,3例患者的小气道功能均有异常。急性发病期进行的肺活检进行了组织学检查、透射电子显微镜检查,2例还进行了免疫荧光检查。存在肺泡内和间质嗜酸性粒细胞性肺炎,伴有闭塞性细支气管炎、微肉芽肿和血管炎。电子显微镜检查显示有大量嗜酸性粒细胞,许多已脱颗粒,还有吞噬嗜酸性粒细胞颗粒和胞质内包涵体的巨噬细胞。1例患者在支气管壁和间质中检测到IgM、IgG和IgA。未检测到IgE或补体。我们认为嗜酸性粒细胞颗粒是造成组织损伤和发热的原因,并提出了相关机制以及对类固醇治疗反应的机制。