牛II型全身性糖原贮积病中的骨骼肌α-葡萄糖苷酶
Skeletal-muscle alpha-glucosidases in bovine generalized glycogenosis type II.
作者信息
Dorling P R, Howell J M, Gawthorne J M
出版信息
Biochem J. 1981 Aug 15;198(2):409-12. doi: 10.1042/bj1980409.
Abstract
The skeletal muscle of cattle suffering from generalized glycogenosis type II was shown to lack acid alpha-glucosidase (EC 3.2.1.3) activity. Furthermore, there was no evidence of enzymically inactive proteins that cross-reacted with antibodies raised against acid alpha-glucosidase from the muscle of normal animals.
摘要
患II型全身性糖原贮积症牛的骨骼肌显示缺乏酸性α-葡萄糖苷酶（EC 3.2.1.3）活性。此外，没有证据表明存在与针对正常动物肌肉中酸性α-葡萄糖苷酶产生的抗体发生交叉反应的无酶活性蛋白。
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