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Rodent and human acid -glucosidase. Purification, properties and inhibition by antibodies. Investigation in type II glycogenosis.

作者信息

de Barsy T, Jacquemin P, Devos P, Hers H G

出版信息

Eur J Biochem. 1972 Nov 21;31(1):156-65. doi: 10.1111/j.1432-1033.1972.tb02514.x.

DOI:10.1111/j.1432-1033.1972.tb02514.x
PMID:4264446
Abstract
摘要

相似文献

1
Rodent and human acid -glucosidase. Purification, properties and inhibition by antibodies. Investigation in type II glycogenosis.啮齿动物和人类的酸性葡萄糖苷酶。纯化、特性及抗体抑制作用。II型糖原贮积病的研究。
Eur J Biochem. 1972 Nov 21;31(1):156-65. doi: 10.1111/j.1432-1033.1972.tb02514.x.
2
Electrophoretic characterization of acidic and neutral amylo 1-4-glucosidase (acid maltase) in human tissues and evidence for two electrophoretic variants in acid maltase deficiency.人体组织中酸性和中性淀粉1-4-葡萄糖苷酶（酸性麦芽糖酶）的电泳特性及酸性麦芽糖酶缺乏症中两种电泳变异体的证据。
Biochem Biophys Res Commun. 1972 Aug 21;48(4):914-20. doi: 10.1016/0006-291x(72)90695-x.
3
Simultaneous absence of alpha-1,4-glucosidase and alpha-1,6-glucosidase activities (pH 4) in tissues of children with type II glycogen storage disease.II型糖原贮积病患儿组织中同时缺乏α-1,4-葡萄糖苷酶和α-1,6-葡萄糖苷酶活性（pH 4）
Biochemistry. 1970 Mar 17;9(6):1423-8. doi: 10.1021/bi00808a017.
4
Studies of lysosomal alpha-glucosidase. I. Purification and properties of the rat liver enzyme.溶酶体α-葡萄糖苷酶的研究。I. 大鼠肝脏酶的纯化及性质
Biochemistry. 1970 Mar 17;9(6):1403-15. doi: 10.1021/bi00808a015.
5
Acid -glucosidase in amniotic fluid.羊水α-葡萄糖苷酶
Biochem Med. 1973 Feb;7(1):39-51. doi: 10.1016/0006-2944(73)90097-5.
6
Characterization of the molecular defect in infantile and adult acid alpha-glucosidase deficiency fibroblasts.婴儿和成人酸性α-葡萄糖苷酶缺乏症成纤维细胞分子缺陷的特征分析。
J Clin Invest. 1978 Dec;62(6):1264-74. doi: 10.1172/JCI109247.
7
Studies of lysosomal alpha-glucosidase. II. Kinetics of action of the rat liver enzyme.溶酶体α-葡萄糖苷酶的研究。II. 大鼠肝脏酶的作用动力学。
Biochemistry. 1970 Mar 17;9(6):1416-22. doi: 10.1021/bi00808a016.
8
The substrate specificity of acid -glucosidase from rabbit muscle.兔肌肉中酸性葡萄糖苷酶的底物特异性。
Biochem J. 1971 Oct;124(4):701-11. doi: 10.1042/bj1240701.
9
Inhibitory effect of pseudo-aminosugars on oligosaccharide glucosidases I and II and on lysosomal alpha-glucosidase from rat liver.假氨基糖对大鼠肝脏寡糖葡糖苷酶I和II以及溶酶体α-葡糖苷酶的抑制作用。
J Biochem. 1990 Jul;108(1):42-6. doi: 10.1093/oxfordjournals.jbchem.a123160.
10
The maltase, glucoamylase and transglucosylase activities of acid -glucosidase from rabbit muscle.兔肌肉酸性葡萄糖苷酶的麦芽糖酶、葡糖淀粉酶和转葡糖基酶活性
Biochem J. 1971 Oct;124(4):713-24. doi: 10.1042/bj1240713.

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A Personal History of Cystinosis by Dr. Jerry Schneider.《胱氨酸病个人史》，作者杰里·施耐德博士。
Cells. 2022 Mar 10;11(6):945. doi: 10.3390/cells11060945.
3
Leaky splicing mutation in the acid maltase gene is associated with delayed onset of glycogenosis type II.
酸性麦芽糖酶基因中的渗漏剪接突变与II型糖原贮积症的延迟发病有关。
Am J Hum Genet. 1995 Apr;56(4):887-97.
4
Skeletal-muscle alpha-glucosidases in bovine generalized glycogenosis type II.牛II型全身性糖原贮积病中的骨骼肌α-葡萄糖苷酶
Biochem J. 1981 Aug 15;198(2):409-12. doi: 10.1042/bj1980409.
5
Immunocytochemistry of lysosomal hydrolases and their precursor forms in normal and mutant human cells.正常和突变人类细胞中溶酶体水解酶及其前体形式的免疫细胞化学研究。
Histochem J. 1984 Sep;16(9):941-54. doi: 10.1007/BF01003850.
6
Demonstration of acid maltase protein in Pompe disease by use of immunohistochemical and enzyme immunoassay methods.运用免疫组织化学和酶免疫测定方法对庞贝病中酸性麦芽糖酶蛋白进行检测。
J Inherit Metab Dis. 1983;6(3):131-2. doi: 10.1007/BF01800747.
7
Glycogen storage diseases in animals and their potential value as models of human disease.动物中的糖原贮积病及其作为人类疾病模型的潜在价值。
J Inherit Metab Dis. 1983;6(1):3-16. doi: 10.1007/BF02391186.
8
Genetic heterogeneity in acid alpha-glucosidase deficiency.酸性α-葡萄糖苷酶缺乏症中的遗传异质性。
Am J Hum Genet. 1983 Jan;35(1):21-33.
9
Immunohistochemical demonstration of acid alpha-glucosidase in muscle in Pompe's disease.庞贝病中肌肉酸性α-葡萄糖苷酶的免疫组织化学显示
Histochem J. 1983 Jun;15(6):601-4. doi: 10.1007/BF01954150.
10
Morquio's disease type A: absence of material cross reacting with antibodies against N-acetylgalactosamine-6-sulfate sulfatase.A型黏多糖贮积症Ⅳ型：缺乏与抗N-乙酰半乳糖胺-6-硫酸酯硫酸酯酶抗体发生交叉反应的物质。
Hum Genet. 1980;54(1):87-91. doi: 10.1007/BF00279054.