Witlin L T, Gadacz T R, Zuidema G D, Kridelbaugh W W
Surgery. 1982 Feb;91(2):205-9.
Caroli's disease, defined as a congenital cystic dilatation of the intrahepatic segmental bile ducts, has responded poorly to conventional methods of treatment. Medical treatment has not been useful, and the various surgical procedures that have been proposed have met with limited success. The course of this disease is characterized by recurrent episodes of cholangitis, liver failure, and hemorrhage from esophageal varices. Two cases of Caroli's disease are presented. Both failed to respond to standard forms of internal and/or external drainage. However, one of the patients has been asymptomatic for 4 years after insertion of a silicone rubber transhepatic stent, despite suffering from recurrent cholangitis and other symptoms for more than 20 years previously. We therefore propose the use of a silicone rubber transhepatic stent as a possible approach to the treatment problem posed by Caroli's disease.
卡罗里病，定义为肝内段胆管的先天性囊性扩张，对传统治疗方法反应不佳。药物治疗无效，所提出的各种外科手术取得的成功有限。该疾病的病程特点是胆管炎反复发作、肝衰竭以及食管静脉曲张出血。本文介绍了两例卡罗里病病例。两者对标准形式的内引流和/或外引流均无反应。然而，其中一名患者在植入硅橡胶经肝支架后4年一直无症状，尽管此前20多年一直患有复发性胆管炎和其他症状。因此，我们建议使用硅橡胶经肝支架作为解决卡罗里病所带来的治疗问题的一种可能方法。
