Quimby S R, Perry H O
J Am Acad Dermatol. 1982 May;6(5):856-61. doi: 10.1016/s0190-9622(82)70075-1.
Nine patients with plaquelike cutaneous mucinosis, including the three described originally in 1960, are presented. The clinical manifestations of asymptomatic persistent, erythematous, infiltrated papules, either isolated or coalescing into plaques, in the midline of the back or chest are suggestive of the diagnosis. The dermal histopathologic findings of perivascular and periappendageal round cell infiltrates and mucin (acid mucopolysaccharides) on special stains confirm the diagnosis. This syndrome is more common among women, may be aggravated by exposure to ultraviolet light, and may subside spontaneously after long periods. We believe the condition of these patients is identical to that described as reticular erythematous mucinosis syndrome.
本文报告了9例斑块状皮肤粘蛋白病患者，其中包括1960年最初描述的3例。临床表现为背部或胸部中线出现无症状的持续性红斑浸润性丘疹，可为孤立性或融合成斑块，提示该诊断。真皮组织病理学表现为血管周围和附属器周围有圆形细胞浸润，特殊染色显示有粘蛋白（酸性粘多糖），证实了该诊断。该综合征在女性中更为常见，暴露于紫外线下可能会加重，长期后可能会自发消退。我们认为这些患者的病情与网状红斑性粘蛋白病综合征相同。
