Reid J M, Coleman E N, Doig W
Br Heart J. 1982 Sep;48(3):236-9. doi: 10.1136/hrt.48.3.236.
Congenital complete atrioventricular block is uncommon, and the outlook is usually regarded as favourable. Thirty-five patients with congenital heart block are presented. There was no obvious sex difference and their ages ranged from 12 days to 85 years, though most were under the age of 20 years when first seen. Accompanying heart disease was noted in six, but presentation with symptoms in early infancy was a more serious risk factor in our experience. Permanent pacing was required in 21, three of whom were neonates. One of the 14 unpaced patients died unexpectedly at the age of 5 years. Long term supervision is necessary, as most will require permanent pacing before their 50th birthday.
先天性完全性房室传导阻滞并不常见,其预后通常被认为良好。本文报告了35例先天性心脏传导阻滞患者。患者无明显性别差异,年龄从12天至85岁不等,但首次就诊时大多数患者年龄在20岁以下。6例伴有心脏病,但根据我们的经验,婴儿早期出现症状是一个更严重的危险因素。21例患者需要永久起搏,其中3例为新生儿。14例未起搏患者中有1例在5岁时意外死亡。由于大多数患者在50岁生日前需要永久起搏,因此需要长期监测。