Kitahara T, Miyasaka Y, Ohwada T, Yada K, Mera H
No Shinkei Geka. 1982 Jun;10(6):675-9.
We have reported a case of cervical spontaneous hematomyelia caused by cavernous hemangioma. A 47-year-old woman experienced a sudden onset of pain in the neck on 5 December 1979. One week after the onset she began to have tetraparesis. There was a rapidly increasing weakness of the extremities and she was referred to our department on 25 December 1979. At the time, the positive neurological findings were flaccid tetraplegia, bilateral loss of all sensory perception below the C4 level and urinary retention. Chest x-ray films demonstrated an elevation of right diaphragma. Roentgenograms of the cervical spine were normal. Emergency myelography via cisternal puncture revealed a central filling defect at the level of C3-C5. But there was no displacement of dentate ligament on lateral view, suggesting an intramedullary mass lesion. Laminectomy from C2 to Th1 and evacuation of the intramedullary blood clot at C3-C5 level were performed successfully. Microscopic examination of clots revealed cavernous hemangioma. The postoperative course was uneventful and the patient gradually improved in her motility. In the review of the literature including our case, vascular malformations are the commonest cause of spontaneous hematomyelia. They are found 12 out of 18 cases (Table 1). The symptoms of spontaneous hematomyelia are characterized by sudden onset of pain and rapid development of long tract sign in a previously asymptomatic individual. Operated cases are summarized in table 2. Good operative results are obtained 6 out 9 cases. We will emphasize that in a case of spontaneous hematomyelia with acute progression of transverse myelopathy, early diagnosis and operation are extremely important, and for this purpose, myelography is considered to be one of the most useful examinations.
我们报告了一例由海绵状血管瘤引起的颈椎自发性脊髓出血性梗死病例。一名47岁女性于1979年12月5日突然出现颈部疼痛。发病一周后,她开始出现四肢轻瘫。四肢无力迅速加重,于1979年12月25日转诊至我科。当时,神经系统阳性体征为弛缓性四肢瘫、C4水平以下双侧所有感觉丧失及尿潴留。胸部X线片显示右膈升高。颈椎X线片正常。经小脑延髓池穿刺进行的急诊脊髓造影显示C3 - C5水平有中央充盈缺损。但侧位片齿状韧带无移位,提示髓内占位性病变。成功实施了从C2至Th1的椎板切除术,并清除了C3 - C5水平的髓内血凝块。血凝块的显微镜检查显示为海绵状血管瘤。术后病程顺利,患者运动功能逐渐改善。在包括我们病例在内的文献回顾中,血管畸形是自发性脊髓出血性梗死最常见的原因。在18例中有12例发现血管畸形(表1)。自发性脊髓出血性梗死的症状特点是在先前无症状的个体中突然出现疼痛并迅速发展为长束征。手术病例总结于表2。9例中有6例手术效果良好。我们将强调,对于伴有横贯性脊髓病急性进展的自发性脊髓出血性梗死病例,早期诊断和手术极为重要,为此,脊髓造影被认为是最有用的检查之一。