Slater D N, Grundman M J, Mitchell L
Postgrad Med J. 1982 Jul;58(681):436-8. doi: 10.1136/pgmj.58.681.436.
A case of Turner's syndrome is described associated with bicuspid aortic stenosis and fatal rupture of a thoracic dissecting aortic aneurysm. Histology of the aneurysm showed severe cystic medial necrosis. This association has not been previously described in the absence of coarctation. In view of the possibility of surgical repair, dissecting aortic aneurysm should be considered in all patients with Turner's syndrome presenting with chest pain, irrespective of the presence or absence of coarctation.
本文描述了一例特纳综合征患者，其合并二叶式主动脉瓣狭窄及胸段主动脉夹层动脉瘤破裂致死。动脉瘤组织学检查显示严重的囊性中层坏死。这种关联在无主动脉缩窄的情况下此前尚未见报道。鉴于手术修复的可能性，对于所有出现胸痛的特纳综合征患者，无论有无主动脉缩窄，均应考虑主动脉夹层动脉瘤的可能。
