Danielson G K, Fuster V
Ann Surg. 1982 Oct;196(4):499-504. doi: 10.1097/00000658-198210000-00014.
Ebstein's anomaly is a complex malformation that has been treated by various surgical techniques, with variable results, since 1958. In 1972, the authors developed a repair that consisted of plication of the free wall of the atrialized portion of the right ventricle, posterior tricuspid anuloplasty, and right atrial reduction. The repair is based on the construction of a monocusp valve by the use of the anterior leaflet of the tricuspid valve, which is usually enlarged in this anomaly. Not all patients are candidates for this procedure, however, because of significant abnormalities of the anterior leaflet such as inadequate size or attachment of the free edge of the leaflet to the ventricular wall. This report describes a ten-year experience with surgical repair of Ebstein's anomaly.
埃布斯坦畸形是一种复杂的畸形，自1958年以来已采用多种手术技术进行治疗，结果各异。1972年，作者开发了一种修复方法，包括右心室心房化部分游离壁的折叠、三尖瓣后瓣环成形术和右心房缩小术。该修复基于利用三尖瓣前叶构建单叶瓣膜，在这种畸形中前叶通常会增大。然而，并非所有患者都适合该手术，因为前叶存在明显异常，如尺寸不足或瓣叶游离缘与心室壁的附着异常。本报告描述了埃布斯坦畸形手术修复的十年经验。
