Kauten J R, Zook E G, Kumar A A, Kinkead L R
Ann Plast Surg. 1982 Oct;9(4):337-43. doi: 10.1097/00000637-198210000-00014.
A case describing primary closure after full-thickness excision of long-standing familial benign chronic pemphigus (Hailey-Hailey disease) in a 54-year-old man is presented. The involved axillary, inguinoscrotal, and perineal skin was excised and closed primarily without difficulty. Eradication of the disease in the excised areas was accomplished with minimal hospitalization and morbidity. Familial benign chronic pemphigus and its differential diagnosis are discussed and the literature on surgical management of this rare disease is reviewed.
本文介绍了一例54岁男性患者，对其长期存在的家族性良性慢性天疱疮（黑利-黑利病）进行全层切除后一期缝合的病例。受累的腋窝、腹股沟阴囊及会阴皮肤被切除并顺利进行了一期缝合。切除区域的疾病得以根除，住院时间和发病率降至最低。文中讨论了家族性良性慢性天疱疮及其鉴别诊断，并对有关这种罕见疾病手术治疗的文献进行了综述。
