Lichtenstern-Peters E, Bein G, Lange L, Jimenez E, Schachinger H, Schartl S, Stoltenburg-Didinger G
Z Kardiol. 1982 Nov;71(11):779-83.
Case report of an infant who, having been under cardiological observation since birth, developed the clinical symptoms of primary pulmonary hypertension at 12 months. The ECC showed right-ventricular hypertrophy, which progressed rapidly. Heart catheterization confirmed the suspected diagnosis of pulmonary hypertension without cardiovascular malformation. Treatment with isoproterenol and tolazoline was initiated but was unsuccessful: the child died at 18 months. The diagnosis was supported by the histopathology.
一名自出生起就接受心脏科观察的婴儿病例报告，该婴儿在12个月时出现原发性肺动脉高压的临床症状。心电图显示右心室肥大，且进展迅速。心导管检查证实了肺动脉高压的疑似诊断，无心血管畸形。开始使用异丙肾上腺素和妥拉唑啉治疗，但未成功：该儿童于18个月时死亡。组织病理学支持该诊断。
