• 文献检索
  • 文档翻译
  • 深度研究
  • 学术资讯
  • Suppr Zotero 插件Zotero 插件
  • 邀请有礼
  • 套餐&价格
  • 历史记录
应用&插件
Suppr Zotero 插件Zotero 插件浏览器插件Mac 客户端Windows 客户端微信小程序
定价
高级版会员购买积分包购买API积分包
服务
文献检索文档翻译深度研究API 文档MCP 服务
关于我们
关于 Suppr公司介绍联系我们用户协议隐私条款
关注我们

Suppr 超能文献

核心技术专利:CN118964589B侵权必究
粤ICP备2023148730 号-1Suppr @ 2026

文献检索

告别复杂PubMed语法,用中文像聊天一样搜索,搜遍4000万医学文献。AI智能推荐,让科研检索更轻松。

立即免费搜索

文件翻译

保留排版,准确专业,支持PDF/Word/PPT等文件格式,支持 12+语言互译。

免费翻译文档

深度研究

AI帮你快速写综述,25分钟生成高质量综述,智能提取关键信息,辅助科研写作。

立即免费体验

Thrombotic thrombocytopenic purpura and hemolytic-uremic syndrome in HLA-identical siblings.

作者信息

Hellman R M, Jackson D V, Buss D H

出版信息

Ann Intern Med. 1980 Aug;93(2):283-4. doi: 10.7326/0003-4819-93-2-284.

DOI:10.7326/0003-4819-93-2-284
PMID:7190807
Abstract

Thrombotic thrombocytopenic purpura and hemolytic-uremic syndrome occurred 6 1/2 years apart in HLA-identical brothers. This unique occurrence supports the concept that the two disorders may be varieties of a basic disease process and suggests the possibility of an inherited predisposition for them.

摘要

相似文献

1
Thrombotic thrombocytopenic purpura and hemolytic-uremic syndrome in HLA-identical siblings.
Ann Intern Med. 1980 Aug;93(2):283-4. doi: 10.7326/0003-4819-93-2-284.
2
Thrombotic thrombocytopenic purpura and haemolytic uraemic syndrome in three siblings.三名兄弟姐妹患血栓性血小板减少性紫癜和溶血性尿毒症综合征。
Arch Dis Child. 1988 Jun;63(6):644-6. doi: 10.1136/adc.63.6.644.
3
von Willebrand factor-cleaving protease in thrombotic thrombocytopenic purpura and the hemolytic-uremic syndrome.血栓性血小板减少性紫癜和溶血尿毒综合征中的血管性血友病因子裂解蛋白酶
N Engl J Med. 1998 Nov 26;339(22):1578-84. doi: 10.1056/NEJM199811263392202.
4
[Hereditary hemolytic uremic syndromes and thrombotic thrombocytopenic purpura].[遗传性溶血性尿毒症综合征与血栓性血小板减少性紫癜]
Nephrol Ther. 2006 Jan;2 Suppl 2:S149-61.
5
Hypocomplementemia discloses genetic predisposition to hemolytic uremic syndrome and thrombotic thrombocytopenic purpura: role of factor H abnormalities. Italian Registry of Familial and Recurrent Hemolytic Uremic Syndrome/Thrombotic Thrombocytopenic Purpura.补体减少揭示了溶血性尿毒症综合征和血栓性血小板减少性紫癜的遗传易感性:H因子异常的作用。意大利家族性和复发性溶血性尿毒症综合征/血栓性血小板减少性紫癜登记处。
J Am Soc Nephrol. 1999 Feb;10(2):281-93. doi: 10.1681/ASN.V102281.
6
Familial and recurrent forms of hemolytic uremic syndrome/thrombotic thrombocytopenic purpura.
Contrib Nephrol. 2001(136):125-39. doi: 10.1159/000060183.
7
Thrombotic thrombocytopenic purpura and hemolytic uremic syndrome: will recent insight into pathogenesis translate into better treatment?
Transfusion. 2002 Apr;42(4):388-92. doi: 10.1046/j.1525-1438.2002.00080.x.
8
Two novel ADAMTS13 gene mutations in thrombotic thrombocytopenic purpura/hemolytic-uremic syndrome (TTP/HUS).血栓性血小板减少性紫癜/溶血性尿毒症综合征(TTP/HUS)中的两种新型ADAMTS13基因突变。
Kidney Int. 2004 Sep;66(3):955-8. doi: 10.1111/j.1523-1755.2004.00841.x.
9
[Familial, recurring plasma infusion dependent thrombotic thrombocytopenic purpura/hemolytic uremic syndrome].
Pol Merkur Lekarski. 2000 Apr;8(46):289-90.
10
The genetics and pathogenesis of haemolytic uraemic syndrome and thrombotic thrombocytopenic purpura.溶血性尿毒症综合征和血栓性血小板减少性紫癜的遗传学及发病机制。
Curr Opin Nephrol Hypertens. 2002 Jul;11(4):431-5. doi: 10.1097/00041552-200207000-00010.

引用本文的文献

1
Emerging Concepts in Immune Thrombotic Thrombocytopenic Purpura.免疫性血栓性血小板减少性紫癜的新观点。
Front Immunol. 2021 Nov 11;12:757192. doi: 10.3389/fimmu.2021.757192. eCollection 2021.
2
Thrombotic thrombocytopenic purpura associated with pregnancy in two sisters.两姐妹妊娠相关的血栓性血小板减少性紫癜
Postgrad Med J. 1993 Mar;69(809):229-31. doi: 10.1136/pgmj.69.809.229.
3
Racial incidence of hemolytic-uremic syndrome.溶血尿毒综合征的种族发病率。
Pediatr Nephrol. 1995 Jun;9(3):401. doi: 10.1007/BF02254233.
4
Clinicopathological study of pancreatic and ganglioneuroblastoma tumours secreting vasoactive intestinal polypeptide (vipomas).分泌血管活性肠肽的胰腺和神经节神经母细胞瘤(血管活性肠肽瘤)的临床病理研究
Br Med J (Clin Res Ed). 1981 May 30;282(6278):1767-71. doi: 10.1136/bmj.282.6278.1767.
5
[Thrombotic thrombocytopenic purpura].[血栓性血小板减少性紫癜]
Klin Wochenschr. 1985 Feb 4;63(3):123-32. doi: 10.1007/BF01734250.
6
Thrombotic thrombocytopenic purpura and haemolytic uraemic syndrome in three siblings.三名兄弟姐妹患血栓性血小板减少性紫癜和溶血性尿毒症综合征。
Arch Dis Child. 1988 Jun;63(6):644-6. doi: 10.1136/adc.63.6.644.