Lhez J M, Joffre F, Escourrou G
J Urol (Paris). 1980;86(9):709-12.
The authors report the 67th published case of multilocular renal cyst, noting that half of the published cases concerned children. Left lumbar pain led to the discovery of a palpable mass of the lower pole of the left kidney visible at urography. At echotomography, alternation between dense and fluid areas made it possible to eliminate a solitary cyst. Renal arteriography was disturbing by virtue of the persistent slight peripheral hypervascularisation after the injection of angiotensin. Diagnostic doubt and the absence of any clearly defined limit between healthy kidney and pathological kidney led to nephrectomy. Histopathology : a thick capsule separated from the healthy kidney a series of cystic structures with no intercommunication between them, nor with the excretory system. Each cyst was lined with an endotheliform single layer epithelium with no renal tissue in the intercystic fibrous separations. The authors emphasise the difficulty of offering an opinion as to the aetiopathogenesis of this lesion which certain feel to be a dysplasia and others as a transitional form with nephroblastoma.
作者报告了第67例已发表的多房性肾囊肿病例，并指出已发表病例中有一半与儿童有关。左侧腰痛导致发现左肾下极可触及的肿块，尿路造影可见。在超声断层扫描中，致密区和液性区交替出现，从而排除了孤立性囊肿。肾动脉造影显示，注射血管紧张素后外周持续轻微血管增多，令人不安。诊断存在疑问，且健康肾与病肾之间没有明确界限，因此进行了肾切除术。组织病理学检查：一层厚包膜将一系列囊性结构与健康肾分隔开，这些囊性结构彼此之间以及与排泄系统均无相通。每个囊肿内衬一层内皮样单层上皮，囊间纤维间隔内无肾组织。作者强调，对于这种病变的病因发病机制很难给出明确意见，有些人认为这是一种发育异常，而另一些人则认为这是肾母细胞瘤的一种过渡形式。
