Yoshimura K, Oka T, Tada Y, Tokunaga K, Onishi S
Department of Urology, Radiology, Osaka University Medical School, Japan.
Urol Int. 1992;48(3):347-9.
A case of a Japanese 14-month-old male infant with multilocular renal cyst is presented. He was admitted with a chief complaint of an abdominal mass. Although clinically and radiographically multilocular renal cyst in the right kidney was suspected, total nephrectomy was performed because of extreme difficulty of partial nephrectomy and impossibility of complete neglect of malignant cystic tumor. Microscopically, immature glomeruloid tissue, primitive tubules, rhabdomyocytes and nerve fibers were noted. The histological diagnosis of multilocular renal cyst with partially differentiated dysplasia was made. Since the first report by Edmunds in 1892, the etiology of multilocular renal cyst has been discussed for years. In our present case, the pathologic findings suggest that multilocular cystic formation in the right kidney might be the result of developmental disturbances.
本文报告一例14个月大的日本男婴，患有多房性肾囊肿。他因腹部肿块为主诉入院。尽管临床和影像学检查怀疑右肾有多房性肾囊肿，但由于部分肾切除术极其困难且无法完全排除恶性囊性肿瘤，故行全肾切除术。显微镜下可见未成熟的肾小球样组织、原始肾小管、横纹肌细胞和神经纤维。组织学诊断为多房性肾囊肿伴部分分化发育异常。自1892年埃德蒙兹首次报告以来，多房性肾囊肿的病因已讨论多年。在我们目前的病例中，病理结果提示右肾多房性囊肿形成可能是发育障碍的结果。
