Zenny J C, Leclère J, Boccon-Gibod L, Fauré C
J Radiol. 1981 Jan;62(1):43-6.
The authors report a case of diffuse cystic angiomatosis of bone. The follow-up over five years showed a dramatic worsening which has seldom been observed. The roentgenographic aspect of this rare disease seems always similar, but non specific. The pathologic diagnosis is difficult. The bony involvement is due to a widespread vascular dysplasia, and the final diagnosis relies upon the association with other arteriovenous or lymphatic disorders, or with an abnormal lymphogram.
作者报告了一例骨弥漫性囊性血管瘤病。五年的随访显示病情急剧恶化,这种情况很少见。这种罕见疾病的X线表现似乎总是相似的,但不具有特异性。病理诊断困难。骨受累是由于广泛的血管发育异常,最终诊断依赖于与其他动静脉或淋巴疾病的关联,或异常的淋巴造影。