Czeizel A, Mészáros M
Eur J Pediatr. 1981 Mar;136(1):81-5. doi: 10.1007/BF00441716.
All first-degree relatives of 81 index patients with isolated ventricular septal defects were examined cardiologically in sample one. The congenital abnormalities in first-degree relatives of 296 index patients affected ventricular septal defects were studied by questionnaire in sample two. (The relatives reported as having congenital cardiovascular malformations were checked). Ventricular septal defects were found in 3.3% and 1.45% of sibs in samples one and two, respectively. The heritability of isolated VSD was 0.57 +/- 0.22. The familial clustering fitted the multifactorial threshold model well. Other congenital cardiovascular malformations were somewhat higher in first-degree relatives of index patients (1.6% in sample one and 1.2% in sample two) than their expected rates. The occurrence of other congenital abnormalities, however, does not exceed the prevalence at birth in the population.
在样本一中,对81例单纯室间隔缺损的先证者的所有一级亲属进行了心脏检查。在样本二中,通过问卷调查研究了296例患室间隔缺损的先证者的一级亲属中的先天性异常情况(对报告有先天性心血管畸形的亲属进行了核查)。在样本一和样本二中,分别有3.3%和1.45%的同胞患有室间隔缺损。单纯室间隔缺损的遗传度为0.57±0.22。家族聚集性很好地符合多因素阈值模型。其他先天性心血管畸形在先证者的一级亲属中(样本一中为1.6%,样本二中为1.2%)略高于预期发生率。然而,其他先天性异常的发生率并未超过该人群的出生患病率。