Kienzle H F, Vorbach M
Chirurg. 1981 Apr;52(4):241-6.
Congenital lobar emphysema is mainly seen in new-born and young babies. In the first hours or days, symptoms appear such as dyspnea, cyanosis, tachypnea, wheezing, thoracic and epigastric retractions. Later symptoms are faintness, psychomotoric retardation and malformation of the thorax. Etiology and pathogenesis of this emphysema of individual parts of the lung are unclear. The course is paroxysmatic, persistent or chronic. Preferred therapy of choice is the resection of the parts concerned. After operation the prognosis is good.
先天性肺叶气肿主要见于新生儿和幼儿。在最初数小时或数天内，会出现呼吸困难、发绀、呼吸急促、喘息、胸廓和上腹部凹陷等症状。后期症状有乏力、精神运动发育迟缓及胸廓畸形。这种肺部个别部位气肿的病因及发病机制尚不清楚。病程呈阵发性、持续性或慢性。首选治疗方法是切除相关部位。术后预后良好。
