Klippel C H
Postgrad Med. 1981 May;69(5):37-40, 42, 44-5. doi: 10.1080/00325481.1981.11715748.
The adrenal gland and the gonads both originate in the embryonic posterior mesenchyme and secrete steroids. Malfunction in either of them results in certain typical developmental problems. The adrenogenital syndrome resulting from excess androgen production occurs as masculinization in the female and precocious maturation in the male. Adrenal tumor usually has the same presentation; feminizing tumors are rare and usually are malignant. Gonadal problems include enlargement of sex organs, ambiguous genitalia, missing testes, and tumor causing precocious puberty. Endocrine problems must be assessed as early as quickly as possible, particularly cases of ambiguous genitalia, so that a proper sex assignment can be made and treatment instituted before parental attitudes arise that will affect the child later on. Surgical restructuring or removal of unneeded organs often is necessary.
肾上腺和性腺均起源于胚胎期的后间充质并分泌类固醇。它们中的任何一个出现功能障碍都会导致某些典型的发育问题。雄激素分泌过多导致的肾上腺性征异常综合征表现为女性男性化和男性性早熟。肾上腺肿瘤通常有相同的表现;产生女性化作用的肿瘤罕见且通常为恶性。性腺问题包括性器官增大、生殖器模糊、睾丸缺失以及导致性早熟的肿瘤。内分泌问题必须尽早尽快评估,尤其是生殖器模糊的病例,以便能够进行恰当的性别指定并在父母态度形成之前开始治疗,因为父母态度会在日后影响孩子。通常需要进行手术重建或切除不需要的器官。