Vedy J, Fauxpoint B, Labat P, Carrica A, Rivaud C
Med Trop (Mars). 1978 Mar-Apr;38(2):201-6.
Hemoglobinopathies and specially drepanocytosis SS and its heterozygotic form SC are responsible of important pathological changes of retina. These changes caused by ischaemia due to vascular thrombosis are generally silent at their beginning, because of their first development in a peripheral area. They have a tendency to progress towards the posterior pole and to get complicated by hemorrhages and detachment of retina. Their study is still to be completed but these disorders already appear as being an important cause of blindness in the populations concerned by this hemoglobinopathy. Treatment is unsatisfactory.
血红蛋白病,特别是镰状细胞贫血症(SS)及其杂合形式(SC)是视网膜重要病理变化的原因。由血管血栓形成导致的缺血所引起的这些变化,一开始通常没有症状,因为它们最初发生在周边区域。它们倾向于向后极发展,并因视网膜出血和脱离而变得复杂。对它们的研究仍有待完善,但这些疾病已似乎成为受这种血红蛋白病影响人群失明的一个重要原因。治疗效果并不理想。