Schmaltz A A, Feine U, Apitz J
Monatsschr Kinderheilkd (1902). 1978 Nov;126(11):672-6.
Compared to the discrete, solitary or multiple pulmonary arteriovenous fistulas, the type of diffuse telangiectatic arteriovenous anastomoses occurs less frequently. Pathogenetically an association with the morbus Rendu-Osler-Weber and with chronic liver diseases is discussed. Based on the literature, and an own case with an additional patent ductus arteriosus, the clinical features are described. Diagnostic results of pulmonary angiography are less helpful than the dynamic radionuclide perfusion scintigraphy which is of great value in following up the disease. There is no successful therapy.
与离散型、孤立性或多发性肺动静脉瘘相比，弥漫性毛细血管扩张性动静脉吻合的类型较少见。在发病机制上，讨论了其与遗传性出血性毛细血管扩张症及慢性肝病的关联。基于文献及1例合并动脉导管未闭的自身病例，描述了其临床特征。肺血管造影的诊断结果不如动态放射性核素灌注闪烁扫描，后者在疾病随访中具有重要价值。目前尚无成功的治疗方法。
