Takeuchi K, Hara M, Yokota H, Okada J, Akai K
Acta Neurochir (Wien). 1981;59(1-2):79-86. doi: 10.1007/BF01411194.
Both the Moyamoya Phenomenon and occlusion of the internal carotid fork are essential radiological findings in true Moyamoya Disease of unknown aetiology. However, the Moyamoya Phenomenon is often observed in occlusive diseases of the internal carotid bifurcation of known aetiology. The authors recently observed acute development of the unilateral Moyamoya Phenomenon following severe vasospasm of the anterior and middle cerebral arteries due to rupture of an anterior communicating aneurysm. The following four factors have been suspected of contributing to development of the Moyamoya Phenomenon: 1. The chronology of arterial occlusion. 2. Extent and location of occlusion. 3. The cause of occlusion. 4. Anatomical and functional disposition of the basal circulation. As regards the chronology, chronic or slowly progressive arterial stenosis has been thought to be a mandatory factor in development of a Moyamoya network, which plays an important role in the form of collateral channels. However, based on the findings outlined in this paper, the congenital factor may be the most important of the four factors.
烟雾病现象和颈内动脉分叉处闭塞都是病因不明的真性烟雾病的重要影像学表现。然而，烟雾病现象常在病因已知的颈内动脉分叉闭塞性疾病中出现。作者最近观察到，由于前交通动脉瘤破裂导致大脑前动脉和大脑中动脉严重血管痉挛后，单侧烟雾病现象急性出现。以下四个因素被怀疑与烟雾病现象的发生有关：1. 动脉闭塞的时间顺序。2. 闭塞的范围和位置。3. 闭塞的原因。4. 基底循环的解剖和功能状态。关于时间顺序，慢性或缓慢进展性动脉狭窄一直被认为是烟雾病血管网形成的必要因素，烟雾病血管网在侧支循环形成中起重要作用。然而，根据本文所述的研究结果，先天性因素可能是这四个因素中最重要的。
