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多发性骨髓瘤:表现为一种神经系统疾病。

Multiple myeloma: presenting as a neurological disorder.

作者信息

Sen S K, Hunter S B, Dent C A, Green L D

出版信息

J Natl Med Assoc. 1980 Feb;72(2):135-9.

PMID:7365813
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC2552481/
Abstract

A case is reported of multiple myeloma presenting with signs and symptoms of paraplegia in a patient with a history of hypertension and remote cerebral vascular accident. The laboratory findings of hyperproteinemia and uricemia suggest a protein synthesizing abnormality. This case emphasizes that most patients with protein abnormality should be investigated by protein electrophoresis and immunoelectrophoresis.Unusual clinical presentation of multiple myeloma may result in an erroneous diagnosis unless proper investigation in the appropriate line is made.

摘要

报告了一例多发性骨髓瘤病例,该患者有高血压病史和陈旧性脑血管意外,表现为截瘫的体征和症状。高蛋白血症和尿酸血症的实验室检查结果提示蛋白质合成异常。该病例强调,大多数蛋白质异常患者应通过蛋白质电泳和免疫电泳进行检查。多发性骨髓瘤不寻常的临床表现可能导致误诊,除非进行适当的相关检查。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9647/2552481/d1f8339c3382/jnma00034-0055-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9647/2552481/03251770cdbc/jnma00034-0054-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9647/2552481/d1f8339c3382/jnma00034-0055-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9647/2552481/03251770cdbc/jnma00034-0054-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9647/2552481/d1f8339c3382/jnma00034-0055-a.jpg

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1
Multiple myeloma: presenting as a neurological disorder.多发性骨髓瘤:表现为一种神经系统疾病。
J Natl Med Assoc. 1980 Feb;72(2):135-9.
2
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3
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[Oncologic emergency: imminent paraplegia].[肿瘤急症:即将发生的截瘫]
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[Spinal cord injury in multiple myeloma].[多发性骨髓瘤中的脊髓损伤]
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Scintigraphically "cold" bone lesion due to myeloma. Correlation of scintigraphical and histological findings.骨髓瘤所致的骨闪烁造影“冷”性病变。骨闪烁造影与组织学检查结果的相关性。
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本文引用的文献

1
HEAVY CHAIN DISEASE- A NEW DISORDER OF SERUM GAMMA-GLOBULINS : REPORT OF THE FIRST CASE.重链病——一种血清γ球蛋白的新病症:首例病例报告。
Am J Med. 1964 Sep;37:332-50. doi: 10.1016/0002-9343(64)90191-3.
2
PLASMA CELL MYELOMA: GAMMA GLOBULIN SYNTHESIS AND STRUCTURE. A REVIEW OF BIOCHEMICAL AND CLINICAL DATA, WITH THE DESCRIPTION OF A NEWLY-RECOGNIZED AND RELATED SYNDROME, "H-GAMMA-2-CHAIN (FRANKLIN'S) DISEASE.浆细胞骨髓瘤:γ球蛋白的合成与结构。生化与临床数据综述,兼述一种新发现的相关综合征,“H-γ-2链(富兰克林氏)病” 。
Medicine (Baltimore). 1963 Nov;42:357-84.
3
The neuropathy of multiple myeloma.
多发性骨髓瘤的神经病变
J Neurol Neurosurg Psychiatry. 1958 May;21(2):73-88. doi: 10.1136/jnnp.21.2.73.
4
Myeloma proteins and antibodies.骨髓瘤蛋白与抗体。
Am J Med. 1969 Dec;47(6):837-44. doi: 10.1016/0002-9343(69)90198-3.
5
Diverse clinical expression of multiple myeloma--atypical presentations.多发性骨髓瘤的多样临床表型——非典型表现
Am J Med Sci. 1974 Feb;267(2):99-109. doi: 10.1097/00000441-197402000-00004.
6
Malignant disease of the lymphoid system in immunological perspective.从免疫学角度看淋巴系统恶性疾病。
Hum Pathol. 1974 Sep;5(5):567-99. doi: 10.1016/s0046-8177(74)80007-9.
7
Unusual presentations of multiple myeloma.多发性骨髓瘤的不典型表现。
Postgrad Med. 1977 May;61(5):116-21. doi: 10.1080/00325481.1977.11712187.
8
Scintigraphically "cold" bone lesion due to myeloma. Correlation of scintigraphical and histological findings.骨髓瘤所致的骨闪烁造影“冷”性病变。骨闪烁造影与组织学检查结果的相关性。
J Belge Radiol. 1977;60(6):501-4.
9
Immunofluorescent and immunoperoxidase characteristics of IgDlambda myeloma involving the orbit.累及眼眶的IgDλ型骨髓瘤的免疫荧光和免疫过氧化物酶特征
Am J Ophthalmol. 1978 Apr;85(4):485-94. doi: 10.1016/s0002-9394(14)75246-8.
10
Uncommon neurological manifestations of multiple myeloma.
Neurol India. 1977 Sep;25(3):170-5.