红细胞生成性原卟啉病中皮肤原卟啉水平升高。
A high skin protoporphyrin level in erythropoietic protoporphyria.
作者信息
Miura T, Torinuki W, Morihana Y
出版信息
Tohoku J Exp Med. 1980 Jan;130(1):97-100. doi: 10.1620/tjem.130.97.
PMID:7368210
Abstract
A high skin protoporphyrin level (4.36 micrograms/g wet weight) was detected in a 14-year-old girl with erythropoietic protoporphyria who died of protoporphyrin hepatopathy cirrhosis. Excess protoporphyrin was detected in the skin by our assay technique which was assumed to cause severe skin photosensitivity.
摘要
在一名死于原卟啉性肝病肝硬化的14岁红细胞生成性原卟啉病女孩中，检测到高皮肤原卟啉水平（4.36微克/克湿重）。通过我们的检测技术在皮肤中检测到过量原卟啉，推测这会导致严重的皮肤光敏感性。
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