红细胞生成性原卟啉病：青少年原卟啉性肝病、肝硬化及死亡。
Erythropoietic protoporphyria: juvenile protoporphyrin hepatopathy cirrhosis and death.
作者信息
Cripps D J, Gilbert L A, Goldfarb S S
出版信息
J Pediatr. 1977 Nov;91(5):744-8. doi: 10.1016/s0022-3476(77)81027-5.
PMID:911406
Abstract
Severe hepatic cirrhosis and failure in erythropoietic protoporphyria is rare. An 11-year-old boy is described who developed protoporphyrin hepatopathy (protoporphyrin 5.75 mg/gm liver wet weight), cirrhosis, and liver failure and died.
摘要
严重肝硬化和红细胞生成性原卟啉病衰竭较为罕见。本文描述了一名11岁男孩，他出现了原卟啉性肝病（原卟啉含量为5.75毫克/克肝脏湿重）、肝硬化和肝功能衰竭并死亡。
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Erythropoietic protoporphyria: juvenile protoporphyrin hepatopathy cirrhosis and death.红细胞生成性原卟啉病：青少年原卟啉性肝病、肝硬化及死亡。
J Pediatr. 1977 Nov;91(5):744-8. doi: 10.1016/s0022-3476(77)81027-5.
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引用本文的文献
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Protoporphyrin-induced cholestasis in the isolated in situ perfused rat liver.原卟啉诱导的原位灌注大鼠肝脏胆汁淤积
J Clin Invest. 1981 Feb;67(2):385-94. doi: 10.1172/JCI110046.
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Phototoxicity of protoporphyrin as related to its subcellular localization in mice livers after short-term feeding with griseofulvin.在用灰黄霉素短期喂养小鼠后，原卟啉的光毒性与其在小鼠肝脏中的亚细胞定位的关系。
Biochem J. 1981 Jul 15;198(1):67-74. doi: 10.1042/bj1980067.
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An autopsy case of erythropoietic protoporphyria with cholestatic jaundice and hepatic failure, and a review of literature.一例伴有胆汁淤积性黄疸和肝衰竭的红细胞生成性原卟啉症尸检病例及文献复习
Virchows Arch A Pathol Anat Histol. 1981;393(2):123-32. doi: 10.1007/BF00431069.
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Pathogenesis and therapy of liver disease in protoporphyria.原卟啉症中肝脏疾病的发病机制与治疗
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