García Mérida M, Azcárate López J, Miguélez Lago C, García Lorenzo G, López Ruiz P, López Pérez G
An Esp Pediatr. 1978 Dec;11(12):876-81.
The present report is based on three infants with respiratory distress syndrome due to congenital lobar emphysema in two and cystic adenomatoid malformation of the lung in the third. The serious worsening of the respiratory distress in two children prompted a partial pulmonary resection within the first 24 hours of life. A brief description of the clinical, radiological and pathological characteristics of this anomalies is included. Our three patients remain asymptomatic showing a normal development, after a follow-up period of five months in one child and just over two years for the other two. Any neonate showing progressive respiratory distress should have a chest X-ray taken to rule out a lobar emphysema or a severe malformation of the lung leading to abnormal ventilation. The management in this cases should be the immediate resection of the affected pulmonary lobes.
本报告基于三名婴儿，其中两名患有先天性大叶性肺气肿导致的呼吸窘迫综合征，第三名患有肺囊性腺瘤样畸形。两名儿童呼吸窘迫的严重恶化促使在出生后24小时内进行了部分肺切除术。文中包括了对这些异常的临床、放射学和病理学特征的简要描述。在一名儿童随访五个月，另外两名儿童随访两年多后，我们的三名患者仍无症状，发育正常。任何出现进行性呼吸窘迫的新生儿都应进行胸部X光检查，以排除大叶性肺气肿或导致通气异常的严重肺畸形。这种情况下的治疗应是立即切除受影响的肺叶。
