Haller J A, Golladay E S, Pickard L R, Tepas J J, Shorter N A, Shermeta D W
Ann Thorac Surg. 1979 Jul;28(1):33-43. doi: 10.1016/s0003-4975(10)63389-9.
Recently we saw 9 infants with life-threatening respiratory distress. Four patients had bronchogenic cyst, 2 had cystic adenomatoid malformation, and 9 had congenital lobar emphysema. Another group of 14 older children had recurrent infection and hemodynamic abnormalities, which responded to operative intervention. Each child required an appropriate resection following definitive diagnosis. These lesions represent a spectrum of closely related anomalies that arise during an early stage of embryonic lung bud maturation. Bronchoscopy is rarely useful, but special roentgenographic studies, including perfusion scans and arteriography, are usually diagnostic. Our operative experience is used to emphasize the urgency of precise diagnosis and surgical management of this poorly recognized clinical syndrome.
最近我们诊治了9例患有危及生命的呼吸窘迫的婴儿。4例患有支气管源性囊肿，2例患有囊性腺瘤样畸形，9例患有先天性大叶性肺气肿。另一组14名年龄较大的儿童有反复感染和血流动力学异常，经手术干预后病情得到缓解。每个患儿在明确诊断后均需进行适当的切除手术。这些病变代表了一系列在胚胎肺芽成熟早期出现的密切相关的异常情况。支气管镜检查很少有用，但特殊的影像学检查，包括灌注扫描和动脉造影，通常可做出诊断。我们的手术经验旨在强调对这种认识不足的临床综合征进行精确诊断和手术治疗的紧迫性。
